Recent studies support that catatonia may be more common in children and adolescents than previously thought. Catatonia is an acute, severe, potentially life-threatening disorder when accompanied by autonomic dysfunction, that also occurs in children and adolescents. Pediatric catatonia may develop in patients with concurrent medical conditions including lupus and anti-N-methyl-d-aspartic acid (NMDA) receptor encephalitis, psychotic and affective disorders, toxic states, autism spectrum disorders, developmental disorders, tic disorders, posttraumatic conditions, and miscellaneous conditions. Case-reports support benzodiazepines and electroconvulsive therapy (ECT), including maintenance ECT, as safe and effective treatments for pediatric catatonia. Catatonia is a treatable condition that warrants prompt diagnosis and treatment. The DSM-5 changes in the classification of catatonia aim to reduce morbidity and mortality in patients with catatonia and to increase further research.